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Found 40 results
Author
Title
Type
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Year
]
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Author
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Manfredi, Giovanni
[Clear All Filters]
2016
Doczi J
,
Torocsik B
,
Echaniz-Laguna A
,
de Camaret BMousson
,
Starkov A
,
Starkova N
,
Gál A
,
Molnár MJ
,
Kawamata H
,
Manfredi G
et al.
. 2016.
Alterations in voltage-sensing of the mitochondrial permeability transition pore in ANT1-deficient cells.
.
Sci Rep. 6:26700.
Stepanova A
,
Shurubor Y
,
Valsecchi F
,
Manfredi G
,
Galkin A
. 2016.
Differential susceptibility of mitochondrial complex II to inhibition by oxaloacetate in brain and heart.
.
Biochim Biophys Acta. 1857(9):1561-8.
Manfredi G
,
Kawamata H
. 2016.
Mitochondria and endoplasmic reticulum crosstalk in amyotrophic lateral sclerosis.
.
Neurobiol Dis. 90:35-42.
2017
Konrad C
,
Kawamata H
,
Bredvik KG
,
Arreguin AJ
,
Cajamarca SA
,
Hupf JC
,
Ravits JM
,
Miller TM
,
Maragakis NJ
,
Hales CM
et al.
. 2017.
Fibroblast bioenergetics to classify amyotrophic lateral sclerosis patients.
.
Mol Neurodegener. 12(1):76.
Kenny TC
,
Manfredi G
,
Germain D
. 2017.
The Mitochondrial Unfolded Protein Response as a Non-Oncogene Addiction to Support Adaptation to Stress during Transformation in Cancer and Beyond.
.
Front Oncol. 7:159.
Kawamata H
,
Peixoto P
,
Konrad C
,
Palomo G
,
Bredvik K
,
Gerges M
,
Valsecchi F
,
Petrucelli L
,
Ravits JM
,
Starkov A
et al.
. 2017.
Mutant TDP-43 does not impair mitochondrial bioenergetics in vitro and in vivo.
.
Mol Neurodegener. 12(1):37.
Kuszak AJ
,
Espey MGraham
,
Falk MJ
,
Holmbeck MA
,
Manfredi G
,
Shadel GS
,
Vernon HJ
,
Zolkipli-Cunningham Z
. 2017.
Nutritional Interventions for Mitochondrial OXPHOS Deficiencies: Mechanisms and Model Systems.
.
Annu Rev Pathol.
Kawamata H
,
Manfredi G
. 2017.
Proteinopathies and OXPHOS dysfunction in neurodegenerative diseases.
.
J Cell Biol. 216(12):3917-3929.
2018
Stepanova A
,
Konrad C
,
Manfredi G
,
Springett R
,
Ten V
,
Galkin A
. 2018.
The dependence of brain mitochondria reactive oxygen species production on oxygen level is linear, except when inhibited by antimycin A.
.
J Neurochem.
Burstein SR
,
Kim HJeong
,
Fels JA
,
Qian L
,
Zhang S
,
Zhou P
,
Starkov AA
,
Iadecola C
,
Manfredi G
. 2018.
Estrogen receptor beta modulates permeability transition in brain mitochondria.
.
Biochim Biophys Acta.
Palomo GM
,
Granatiero V
,
Kawamata H
,
Konrad C
,
Kim M
,
Arreguin AJ
,
Zhao D
,
Milner TA
,
Manfredi G
. 2018.
Parkin is a disease modifier in the mutant SOD1 mouse model of ALS.
.
EMBO Mol Med.
Anderson CJ
,
Kahl A
,
Qian L
,
Stepanova A
,
Starkov A
,
Manfredi G
,
Iadecola C
,
Zhou P
. 2018.
Prohibitin is a positive modulator of mitochondrial function in PC12 cells under oxidative stress.
.
J Neurochem.
Chen Q
,
Kirk K
,
Shurubor YI
,
Zhao D
,
Arreguin AJ
,
Shahi I
,
Valsecchi F
,
Primiano G
,
Calder EL
,
Carelli V
et al.
. 2018.
Rewiring of Glutamine Metabolism Is a Bioenergetic Adaptation of Human Cells with Mitochondrial DNA Mutations.
.
Cell Metab.
2019
Anderson CJ
,
Bredvik K
,
Burstein SR
,
Davis C
,
Meadows SM
,
Dash J
,
Case L
,
Milner TA
,
Kawamata H
,
Zuberi A
et al.
. 2019.
ALS/FTD mutant CHCHD10 mice reveal a tissue-specific toxic gain-of-function and mitochondrial stress response.
.
Acta Neuropathol.
Deng Z
,
Lim J
,
Wang Q
,
Purtell K
,
Wu S
,
Palomo GM
,
Tan H
,
Manfredi G
,
Zhao Y
,
Peng J
et al.
. 2019.
ALS-FTLD-linked mutations of SQSTM1/p62 disrupt selective autophagy and NFE2L2/NRF2 anti-oxidative stress pathway.
.
Autophagy. :1-15.
Hayes LR
,
Asress SA
,
Li Y
,
Galkin A
,
Stepanova A
,
Kawamata H
,
Manfredi G
,
Glass JD
. 2019.
Distal denervation in the SOD1 knockout mouse correlates with loss of mitochondria at the motor nerve terminal.
.
Exp Neurol. 318:251-257.
Cornacchia D
,
Zhang C
,
Zimmer B
,
Chung SYoung
,
Fan Y
,
Soliman MA
,
Tchieu J
,
Chambers SM
,
Shah H
,
Paull D
et al.
. 2019.
Lipid Deprivation Induces a Stable, Naive-to-Primed Intermediate State of Pluripotency in Human PSCs.
.
Cell Stem Cell.
Granatiero V
,
Manfredi G
. 2019.
Mitochondrial Transport and Turnover in the Pathogenesis of Amyotrophic Lateral Sclerosis.
.
Biology (Basel). 8(2)
Granatiero V
,
Konrad C
,
Bredvik K
,
Manfredi G
,
Kawamata H
. 2019.
Nrf2 signaling links ER oxidative protein folding and calcium homeostasis in health and disease.
.
Life Sci Alliance. 2(5)
Anderson CJ
,
Kahl A
,
Fruitman H
,
Qian L
,
Zhou P
,
Manfredi G
,
Iadecola C
. 2019.
Prohibitin levels regulate OMA1 activity and turnover in neurons.
.
Cell Death Differ.
Fels JA
,
Manfredi G
. 2019.
Sex Differences in Ischemia/Reperfusion Injury: The Role of Mitochondrial Permeability Transition.
.
Neurochem Res.
2020
P Ozdinler H
,
Gautam M
,
Gozutok O
,
Konrad C
,
Manfredi G
,
Gomez EArea
,
Mitsumoto H
,
Erb ML
,
Tian Z
,
Haase G
. 2020.
Better understanding the neurobiology of primary lateral sclerosis.
.
Amyotroph Lateral Scler Frontotemporal Degener. 21(sup1):35-46.
Qu Y
,
Konrad C
,
Anderson C
,
Qian L
,
Yin T
,
Manfredi G
,
Iadecola C
,
Zhou P
. 2020.
Prohibitin S-Nitrosylation Is Required for the Neuroprotective Effect of Nitric Oxide in Neuronal Cultures.
.
J Neurosci. 40(16):3142-3151.
Jenkins ECharles
,
Shah N
,
Gomez M
,
Casalena G
,
Zhao D
,
Kenny TC
,
Guariglia SRose
,
Manfredi G
,
Germain D
. 2020.
Proteasome mapping reveals sexual dimorphism in tissue-specific sensitivity to protein aggregations.
.
EMBO Rep. :e48978.
Jenkins ECharles
,
Casalena G
,
Gomez M
,
Zhao D
,
Kenny TC
,
Shah N
,
Manfredi G
,
Germain D
. 2020.
Raloxifene is a female-specific proteostasis therapeutic in the spinal cord.
.
Endocrinology.
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