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Found 6 results
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Keyword
is
Animals
and
Author
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Manfredi, Giovanni
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C
Sayles NM
,
Napierala JS
,
Anrather J
,
Diedhiou N
,
Li J
,
Napierala M
,
Puccio H
,
Manfredi G
. 2023.
Comparative multi-omic analyses of cardiac mitochondrial stress in three mouse models of frataxin deficiency.
.
Dis Model Mech. 16(10)
D
Stepanova A
,
Shurubor Y
,
Valsecchi F
,
Manfredi G
,
Galkin A
. 2016.
Differential susceptibility of mitochondrial complex II to inhibition by oxaloacetate in brain and heart.
.
Biochim Biophys Acta. 1857(9):1561-8.
G
Nelson AT
,
Cicardi MElena
,
Markandaiah SS
,
Han JYs
,
Philp NJ
,
Welebob E
,
Haeusler AR
,
Pasinelli P
,
Manfredi G
,
Kawamata H
et al.
. 2024.
Glucose hypometabolism prompts RAN translation and exacerbates C9orf72-related ALS/FTD phenotypes.
.
EMBO Rep. 25(5):2479-2510.
M
Manfredi G
,
Kawamata H
. 2016.
Mitochondria and endoplasmic reticulum crosstalk in amyotrophic lateral sclerosis.
.
Neurobiol Dis. 90:35-42.
P
Kawamata H
,
Manfredi G
. 2017.
Proteinopathies and OXPHOS dysfunction in neurodegenerative diseases.
.
J Cell Biol. 216(12):3917-3929.
S
Sasset L
,
Chowdhury KH
,
Manzo OL
,
Rubinelli L
,
Konrad C
,
J Maschek A
,
Manfredi G
,
Holland WL
,
Di Lorenzo A
. 2023.
Sphingosine-1-phosphate controls endothelial sphingolipid homeostasis via ORMDL.
.
EMBO Rep. 24(1):e54689.