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Found 10 results
Author
Title
Type
[
Year
]
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Author
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Kawamata, Hibiki
[Clear All Filters]
2016
Doczi J
,
Torocsik B
,
Echaniz-Laguna A
,
de Camaret BMousson
,
Starkov A
,
Starkova N
,
Gál A
,
Molnár MJ
,
Kawamata H
,
Manfredi G
et al.
. 2016.
Alterations in voltage-sensing of the mitochondrial permeability transition pore in ANT1-deficient cells.
.
Sci Rep. 6:26700.
Manfredi G
,
Kawamata H
. 2016.
Mitochondria and endoplasmic reticulum crosstalk in amyotrophic lateral sclerosis.
.
Neurobiol Dis. 90:35-42.
2017
Konrad C
,
Kawamata H
,
Bredvik KG
,
Arreguin AJ
,
Cajamarca SA
,
Hupf JC
,
Ravits JM
,
Miller TM
,
Maragakis NJ
,
Hales CM
et al.
. 2017.
Fibroblast bioenergetics to classify amyotrophic lateral sclerosis patients.
.
Mol Neurodegener. 12(1):76.
Kawamata H
,
Peixoto P
,
Konrad C
,
Palomo G
,
Bredvik K
,
Gerges M
,
Valsecchi F
,
Petrucelli L
,
Ravits JM
,
Starkov A
et al.
. 2017.
Mutant TDP-43 does not impair mitochondrial bioenergetics in vitro and in vivo.
.
Mol Neurodegener. 12(1):37.
Kawamata H
,
Manfredi G
. 2017.
Proteinopathies and OXPHOS dysfunction in neurodegenerative diseases.
.
J Cell Biol. 216(12):3917-3929.
2018
Palomo GM
,
Granatiero V
,
Kawamata H
,
Konrad C
,
Kim M
,
Arreguin AJ
,
Zhao D
,
Milner TA
,
Manfredi G
. 2018.
Parkin is a disease modifier in the mutant SOD1 mouse model of ALS.
.
EMBO Mol Med.
2019
Anderson CJ
,
Bredvik K
,
Burstein SR
,
Davis C
,
Meadows SM
,
Dash J
,
Case L
,
Milner TA
,
Kawamata H
,
Zuberi A
et al.
. 2019.
ALS/FTD mutant CHCHD10 mice reveal a tissue-specific toxic gain-of-function and mitochondrial stress response.
.
Acta Neuropathol.
Hayes LR
,
Asress SA
,
Li Y
,
Galkin A
,
Stepanova A
,
Kawamata H
,
Manfredi G
,
Glass JD
. 2019.
Distal denervation in the SOD1 knockout mouse correlates with loss of mitochondria at the motor nerve terminal.
.
Exp Neurol. 318:251-257.
McAvoy K
,
Kawamata H
. 2019.
Glial mitochondrial function and dysfunction in health and neurodegeneration.
.
Mol Cell Neurosci. :103417.
Granatiero V
,
Konrad C
,
Bredvik K
,
Manfredi G
,
Kawamata H
. 2019.
Nrf2 signaling links ER oxidative protein folding and calcium homeostasis in health and disease.
.
Life Sci Alliance. 2(5)