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Publications

Found 31 results
Author Title Type [ Year(Asc)]
Filters: Author is Manfredi, Giovanni  [Clear All Filters]
2017
Kawamata H, Peixoto P, Konrad C, Palomo G, Bredvik K, Gerges M, Valsecchi F, Petrucelli L, Ravits JM, Starkov A et al..  2017.  Mutant TDP-43 does not impair mitochondrial bioenergetics in vitro and in vivo.. Mol Neurodegener. 12(1):37.
Kuszak AJ, Espey MGraham, Falk MJ, Holmbeck MA, Manfredi G, Shadel GS, Vernon HJ, Zolkipli-Cunningham Z.  2017.  Nutritional Interventions for Mitochondrial OXPHOS Deficiencies: Mechanisms and Model Systems.. Annu Rev Pathol.
Kawamata H, Manfredi G.  2017.  Proteinopathies and OXPHOS dysfunction in neurodegenerative diseases.. J Cell Biol. 216(12):3917-3929.
2016
Doczi J, Torocsik B, Echaniz-Laguna A, de Camaret BMousson, Starkov A, Starkova N, Gál A, Molnár MJ, Kawamata H, Manfredi G et al..  2016.  Alterations in voltage-sensing of the mitochondrial permeability transition pore in ANT1-deficient cells.. Sci Rep. 6:26700.
Stepanova A, Shurubor Y, Valsecchi F, Manfredi G, Galkin A.  2016.  Differential susceptibility of mitochondrial complex II to inhibition by oxaloacetate in brain and heart.. Biochim Biophys Acta. 1857(9):1561-8.
Manfredi G, Kawamata H.  2016.  Mitochondria and endoplasmic reticulum crosstalk in amyotrophic lateral sclerosis.. Neurobiol Dis. 90:35-42.
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  • About BMRI
    • Our Mission
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    • Campus
    • Ways to Give
    • Administration
  • Faculty & Research
    • Faculty, Primary Appointments
    • Faculty, Secondary Appointments
    • Appel Institute
    • Center for Neurogenetics
    • Clinical & Translational Neuroscience Unit
      • CTNU Director
      • CTNU Research Opportunities
    • Affiliate Institutions
    • New Grants
    • Publications
  • News
    • New Grants
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  • Education
    • Neuroscience Graduate Program
    • Neuroscience Retreat
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    • Medical School AOC
    • First Year Students
  • Core Facilities
    • Neuroanatomy EM Core
    • Neurogenetic Repository
    • BMRI Cores
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    • BMRI Diversity and Inclusion
    • Emerging Leaders in Neuroscience
    • BMRI Summer Scholars Program
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